I now have all the data needed for a comprehensive, illustrated answer. Let me compile it.
Developmental Dysplasia of the Hip (DDH)
DDH describes a spectrum of hip instability ranging from a shallow (dysplastic) acetabulum that may sublux, to a fully dislocated hip that is irreducible. The key underlying problem is failure of normal concentric development between the femoral head and the acetabulum.
Spectrum of Disease
| Grade | Description |
|---|
| Dysplasia | Shallow acetabulum; femoral head in joint but inadequately covered |
| Subluxation | Femoral head partially displaced, within the labrum |
| Dislocation (reducible) | Ortolani positive — dislocated but reducible |
| Dislocation (irreducible) | Ortolani negative — dislocated and cannot be reduced |
| Teratologic | Dislocated in utero, irreducible at birth; associated with arthrogryposis, Larsen syndrome, trisomy 21 |
Incidence & Risk Factors
- Neonatal instability: ~20 per 1,000 live births; true dislocation ~2 per 1,000
- Many hips stabilise spontaneously within the first 2–3 weeks
Risk factors (in decreasing importance):
- Breech presentation (especially extended breech) — 30–50× increased risk
- Female sex — 4–5× more common; oestrogen-related peripartum ligamentous laxity
- Positive family history — ≥20% incidence with affected first-degree relative
- Firstborn child — tight primigravid uterus, left occipito-anterior position → 67% left hip
- Oligohydramnios — restricts fetal movement
- Swaddling with hips in extension — postnatal risk factor
Associations: torticollis (20%), metatarsus adductus (10%); no association with clubfoot.
Diagnosis
Clinical Examination — Neonate
The critical question at neonatal examination:
Is the hip dislocated? If so, is it reducible (Ortolani +) or irreducible? If not dislocated, is it dislocatable (Barlow +)?
Figure: (a) Ortolani test — elevation and abduction of the femur causes a palpable clunk as the dislocated femoral head reduces. (b) Barlow test — adduction and posterior depression causes a palpable clunk as the hip dislocates.
Ortolani test: Hip at 90° flexion → gentle abduction + elevation of greater trochanter → clunk of reduction = positive (dislocated but reducible)
Barlow test: Hip at 90° flexion → adduction + posterior pressure on knee → clunk of dislocation = positive (reduced but dislocatable)
Bilateral dislocation may be missed — abduction is symmetrically limited and may appear normal in low-tone infants.
Clinical Examination — Older Infant/Child
| Sign | Age | Finding |
|---|
| Limited hip abduction | > 3 months | < 60° abduction on affected side |
| Galeazzi sign | Any | Apparent femoral shortening — knees at unequal heights with hips & knees at 90° |
| Asymmetric thigh/gluteal folds | Infant | Less reliable |
| Trendelenburg gait | Toddler | Contralateral pelvis drops when standing on affected leg |
| Limping / tip-toe gait | Child | Affected leg appears short |
| Lumbar lordosis + waddling gait | Bilateral | |
| Exercise-related groin/knee pain | Adolescent | |
Investigations
1. Ultrasound (< 4–6 months)
Modality of choice in the neonatal period, since the femoral head is cartilaginous and not visible on X-ray until 4–6 months.
Performed at 4–6 weeks of age (coronal view, lateral decubitus position):
Graf Classification (α angle on coronal US):
| Graf Type | α angle | Interpretation | Action |
|---|
| I | ≥ 60° | Normal, mature | None |
| IIa | 50–59° | Immature (< 3 months) | Follow-up |
| IIb | 50–59° | Delayed ossification (> 3 months) | Treatment |
| IIc | 43–49° | Critical zone — borderline | Treatment |
| III | < 43° | Subluxed; cartilaginous roof displaced | Treatment |
| IV | — | Dislocated | Treatment |
Normal: α > 60°; femoral head bisected by the iliac line; Morin index (femoral head coverage) > 50%.
A: Graf type IV hip (dislocated). B: After Pavlik harness — α angle 62° (Graf type I — normalised). C: Follow-up X-ray at 6 months showing recurrent acetabular dysplasia (AI = 28°). D: After abduction bracing — AI normalised to 20°.
Selective US screening is recommended for:
- Breech presentation
- Positive family history
- Abnormal clinical examination
2. Plain Radiograph (≥ 4–5 months)
Used once the femoral ossific nucleus begins to appear (normally 4–6 months; often delayed in DDH).
Right hip normal; left hip dislocated. The ossific nucleus should lie in the inferomedial quadrant.
Key radiographic lines and measurements:
| Line / Measurement | Description | Normal |
|---|
| Hilgenreiner's line | Horizontal line through both triradiate cartilages (Y-cartilages) | Reference line |
| Perkin's line | Vertical line through lateral acetabular edge, perpendicular to Hilgenreiner's | Ossific nucleus should be medial |
| Shenton's line | Smooth arc from femoral neck to superior pubic ramus | Disrupted in dislocation/subluxation |
| Acetabular index (AI) | Angle between Hilgenreiner's line and roof of acetabulum | Normal: < 25–30° (decreases with age) |
| Centre-edge (Wiberg) angle | In older children — lateral femoral head coverage | Normal > 25° |
3. Arthrography
Used intraoperatively to:
- Confirm concentric reduction before casting
- Identify blocks to reduction (the "thorn sign" indicates normal labral position)
- Assess medial dye pool width (> 8 mm suggests inadequate reduction)
4. CT / MRI
- Post-reduction confirmation of concentric reduction in the spica cast
- MRI preferred (no radiation) for post-reduction assessment
- CT used where MRI unavailable
Blocks to Concentric Reduction
When a hip cannot be reduced, the following structures are implicated:
Structures blocking reduction: iliopsoas tendon (hourglass constriction), pulvinar (fibrofatty tissue), redundant ligamentum teres, transverse acetabular ligament, contracted inferomedial capsule, inverted/everted labrum.
Treatment
The overarching goal is stable concentric reduction of the femoral head within the acetabulum, achieved as early as possible to allow normal acetabular development — while avoiding avascular necrosis (AVN) of the femoral head, the most feared complication.
Age 0–6 Months: Pavlik Harness
The anterior strap controls hip flexion (~100°). The posterior strap limits adduction and encourages abduction.
- First-line treatment for all Ortolani-positive and Barlow-positive hips (reducible and dislocatable)
- Maintains hips in the "human position" — ~100° of flexion, mild abduction (Salter position)
- Worn 23 hours/day for at least 6 weeks after reduction achieved, then part-time (nights/naps) for a further 6–8 weeks
- Reduction confirmed by ultrasound after fitting; repeat US to monitor
Safe zone (Ramsey zone): Between maximum adduction before redislocation and maximum abduction before AVN risk. A narrow safe zone (< 40°) is an indication for adductor tenotomy.
Complications of Pavlik harness:
- AVN — from excessive abduction (compresses posterosuperior retinacular branch of medial femoral circumflex artery)
- Femoral nerve palsy — from excessive flexion (transient)
- "Pavlik disease" — if reduction is not achieved within 3 weeks, continued harness use causes erosion of the pelvis superior to the acetabulum, making subsequent closed reduction more difficult → discontinue at 3 weeks if not reduced
Risk factors for harness failure:
- Age > 7 weeks at initiation
- Bilateral dislocations
- Absent Ortolani sign (irreducible hip)
- Teratologic dislocation (absolute contraindication)
Age 6–18 Months: Closed Reduction + Spica Cast
For hips failing Pavlik harness treatment, or presenting in this age group.
Procedure (under general anaesthetic):
- Examination under anaesthetic
- Hip arthrography — assess reduction and blocks
- Adductor ± psoas tenotomy if tight
- Closed reduction — gentle traction + flexion + abduction
- Hip spica cast in the stable zone of abduction (hips ≥ 90° flexion)
- Post-reduction CT or MRI to confirm concentric reduction
If closed reduction fails or only achieved in extreme position → proceed to open reduction.
Age 6–18 Months (failed closed) / Age ≥ 18 Months: Open Reduction
Approach:
- Medial approach (Ferguson/Ludloff): 6–24 months; allows direct access to medial obstacles; does not permit simultaneous capsulorrhaphy
- Anterior (Smith-Petersen) approach: preferred from 9–12 months onwards; allows capsulorrhaphy; lower risk to medial femoral circumflex artery than medial approach at older ages
Structures released at open reduction:
- Adductor longus tenotomy
- Iliopsoas release
- Pulvinar excision
- Transverse acetabular ligament division
- Labrum repositioning
- Capsulorrhaphy (tightening of capsule) to maintain reduction
Femoral shortening osteotomy: Added for children > 18 months to reduce excessive pressure on reduction (reduces AVN risk).
Pelvic Osteotomies (for residual acetabular dysplasia)
| Osteotomy | Age | Mechanism |
|---|
| Salter | 18 months–6 years | Single innominate osteotomy; redirects acetabulum anterolaterally; requires open triradiate cartilage |
| Pemberton | 18 months–8 years | Incomplete pericapsular osteotomy; reduces acetabular volume; good for large femoral heads |
| Dega | Similar to Pemberton | Posterior hinge; useful in neuromuscular DDH |
| Triple osteotomy (Steel/Tönnis) | Older children, skeletal near-maturity | Three cuts (ilium, ischium, pubis); triradiate cartilage must be closed or near-closed |
| Periacetabular (Ganz/PAO) | Adolescent/adult; closed triradiate | Redirects entire acetabulum; best for reducible dysplastic hips; preserves posterior column |
| Chiari | Salvage | Medial displacement osteotomy; non-anatomic; used for irreducible dysplasia |
| Shelf/augmentation | Salvage | Extends acetabular roof with bone graft |
Surgery is contraindicated in children > 6–8 years with bilateral dislocations and > 8–10 years with unilateral — the pseudoacetabulum provides sufficient function and correction risks more harm than benefit.
Summary Treatment Algorithm
Birth → Neonatal exam (Ortolani / Barlow)
│
├─ Unstable / dislocated → Observe 2–3 weeks (many resolve spontaneously)
│ Still abnormal at 4–6 weeks → Ultrasound + Pavlik harness
│
├─ 0–6 months → Pavlik harness (23 h/day x 6–8 weeks)
│ Reduced → Continue until US/XR normal
│ Not reduced in 3 weeks → Stop harness → EUA + closed reduction + spica
│
├─ 6–18 months → EUA + arthrogram + closed reduction + spica cast
│ Failure → Open reduction (medial or anterior approach) ± adductor tenotomy
│
├─ 18 months–3 years → Open reduction + femoral shortening + possible pelvic osteotomy
│
├─ 3–8 years → Open reduction + pelvic osteotomy (Salter/Pemberton/Dega)
│
├─ Older child / adolescent → Triple/PAO osteotomy ± femoral osteotomy
│
└─ Adult → PAO (if reducible), Chiari/shelf (salvage), or THA when arthritic
Complications
| Complication | Cause | Comments |
|---|
| Avascular necrosis (AVN) | Excessive abduction, forced reduction, medial approach | Most feared; graded I–V; can lead to permanent deformity and early OA |
| Redislocation | Inadequate capsulorrhaphy or reduction | Requires repeat intervention |
| Residual acetabular dysplasia | Incomplete treatment response | May need pelvic osteotomy |
| Femoral nerve palsy | Excessive flexion in Pavlik harness | Transient; resolves on harness adjustment |
| Leg length discrepancy | AVN or growth disturbance | — |
| Early osteoarthritis | Untreated or poorly treated DDH | Leads to THA in adult life |
| "Pavlik disease" | Continued harness when not reducing | Acetabular erosion; complicates later reduction |
Sources: Miller's Review of Orthopaedics, 9th ed.; Bailey and Love's Short Practice of Surgery, 28th ed.; Schwartz's Principles of Surgery, 11th ed.; Grainger & Allison's Diagnostic Radiology