Plain-language summary
This CT confirms D-transposition of the great arteries (D-TGA), a significant congenital heart condition in which the two main arteries arise from the wrong pumping chambers:
- The aorta arises from the right ventricle instead of the left ventricle.
- The pulmonary artery arises from the left ventricle instead of the right ventricle.
- The heart’s upper-to-lower chamber connections are normal, but the ventricle-to-artery connections are reversed. This is what the report means by “atrioventricular concordance” and “ventriculo-arterial discordance.”
In D-TGA, blood flow to the body and lungs tends to run in parallel rather than in the usual series. Openings between chambers can permit mixing of oxygen-poor and oxygen-rich blood, which is necessary for survival before definitive repair.
Cincinnati Children’s explanation describes this circulation pattern.
Findings in this report
| Finding | What it means |
|---|
| D-TGA | The main diagnosis, with the aorta coming from the right ventricle and pulmonary artery from the left ventricle. |
| ASD | A hole between the upper chambers. It permits some mixing of blood. |
| Subpulmonic VSD | A hole between the lower chambers, located beneath the pulmonary valve/outflow. It also permits mixing and is highly relevant to surgical planning. |
| Narrow pulmonary outflow and small pulmonary arteries | The pathway to the lungs is narrowed, and both branch pulmonary arteries are relatively small. This can reduce blood flow to the lungs and contribute to low oxygen levels/cyanosis. |
| McGoon ratio 1.6 | A measurement of pulmonary artery size used by congenital heart surgeons. A value of 1.6 suggests the pulmonary arteries are small/borderline and must be factored into the choice and timing of repair. It is not a result that should be interpreted alone. |
| Mediastinal aortopulmonary collaterals | Small extra vessels have formed between the body circulation and lung circulation. They often develop when normal pulmonary blood flow has been limited. |
| Double SVC | There are two superior vena cavae: the usual right SVC and a left SVC draining through the coronary sinus into the right atrium. This is usually manageable but matters during surgery/catheter procedures. |
| Right atrium enlarged and right ventricle hypertrophied | The right ventricle is working as the main pumping chamber to the body, so it has become thicker. |
| Normal pulmonary veins | The veins from the lungs drain normally into the left atrium. This is favorable. |
| Normal left-sided aortic arch, no coarctation | No narrowing of the aorta was seen. This is favorable. |
| No PDA | The ductus arteriosus is closed. |
| Coronary arteries not adequately seen | An important limitation. Coronary anatomy is essential before choosing an operation, so the cardiology/surgical team may need echocardiography, catheterization, or better coronary imaging. |
Overall interpretation
This is complex D-TGA with an ASD, a subpulmonic VSD, and obstruction/narrowing of the path to the pulmonary arteries, along with relatively small but connected branch pulmonary arteries. The extra aortopulmonary collateral vessels support the impression that lung blood flow has been restricted.
The favorable features are:
- Normal pulmonary venous drainage
- No aortic coarctation
- No aortic override
- Branch pulmonary arteries are confluent, meaning they are connected to each other rather than discontinuous
The key concerns are:
- Narrow pulmonary outflow
- Small pulmonary arteries
- VSD anatomy
- Coronary arteries not clearly defined
- Need to determine the best definitive repair for this exact anatomy
This does not automatically mean one specific surgery. In straightforward D-TGA, an arterial switch is commonly used, but when there is VSD plus pulmonary outflow obstruction, the repair may need a different or staged surgical strategy. The choice depends on detailed echo/catheter findings, the exact VSD-to-aorta relationship, valve sizes, pulmonary artery growth, and coronary anatomy. The report’s instruction to correlate with echocardiography is important.
What to discuss urgently with the pediatric cardiologist/cardiac surgeon
- What is her current oxygen saturation at rest, feeding, and crying?
- How severe is the pulmonary outflow obstruction on Doppler echocardiography, including the pressure gradient?
- Is the VSD suitably positioned for an intracardiac repair?
- Are the pulmonary arteries large enough for the planned repair, or is an interim procedure needed?
- How will the coronary arteries be defined before surgery?
- What is the proposed operation, timing, and whether catheterization is required first?
Seek emergency care now if she has
- Blue lips/tongue or worsening blueness
- Fast or labored breathing
- Poor feeding, sweating with feeds, vomiting, or markedly reduced urine output
- Extreme sleepiness, limpness, fainting, or irritability
- Oxygen saturation below the target set by her pediatric cardiologist
This report describes a condition that needs close management by a pediatric congenital-heart surgical team, rather than routine follow-up.